Abstract

Olfactory neuroblastoma is an uncommon malignant nasal tumor that originates from neuroepithelial cells of the nasal cavity. It is an embryonal neuroendocrine tumor that originates from neural crest progenitor cells. Olfactory neuroblastoma may infiltrate the sinuses, orbit, and cranium through the nasal cavity. This tumor is characterized by a pattern of slow growth and local recurrence. In pediatric age this tumor is even rarer, with an estimated incidence of 0.1 per 100,000 children up to 15 years. Treatment options are surgical excision or surgery combined with radiotherapy and/or chemotherapy. The present study reports the case of a 1.5-year-old female patient having olfactory neuroblastoma, presenting with a mass in the left nasal cavity.

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