Abstract

Adenoid cystic carcinoma (ACC) of the vagina arising from Bartholin’s glands is a rare type of female malignancy. ACC of the vulva is rare, and treatment protocols are often based on experience with similar tumours in other locations (e.g. head and neck) and case reports. Here, we report a case of a 52-year-old female patient who presented with a pain above perineum and lower end of vagina leading to a diagnosis of ACC of the vagina after biopsy and confirmation on immunohistochemical analysis. Often, such lesion is clinically misdiagnosed as a cyst or inflammation. The present case was clinically suscpected to be either a bartholin cyst or lipoma or parasitic fibroid or calcification. The possibility of cancer should be considered in any female older than 40 years of age with a lesion near the Bartholin’s glands.

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