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One and a Half Ventricle Repair of a Rare Ebstenoid Tricuspid Valve Orifice with a Hypoplastic Right Ventricle

Ranajit B Naik, Divya Mangal, Ankit Mathur

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Journal of Cardiovascular Medicine and Surgery 10(3-4):p 84-88, July -Dec. 2024. | DOI: http://dx.doi.org/10.21088/jcms.2454.7123.103424.5

How Cite This Article:

Naik RB, Mangal D, Mathur A. Journal: Journal of Cardiovascular Medicine and Surgery Publication Date: July–December 2024 Volume/Issue: 10(3-4): 84-88

Timeline

Received : September 24, 2024         Accepted : November 13, 2024          Published : December 29, 2024

Abstract

Primary tricuspid valve disease related to its congenital malformation is rare. Ebstein’s anamoly is a rare congenital condition affecting the septal and posterior leaflets of the tricuspid valve. Ebstein’s anamoly has a wide spectrum of pathological features. We describe the case of 33 year old female with Ebsteinoid tricuspid valve orifice, severely hypoplastic right ventricle and thrombus in a giant right atrium, with intact interatrial and interventricular septa. The patient was managed surgically with Kays tricuspid annuloplasty and right Bidirectional Glenn anastomosis constituting one and a half ventricular repair with satisfactory outcome.


References

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There are no additional data available.

Funding

This research received no funding.

Author Contributions

All authors contributed significantly to the work and approve its publication.

Ethics Declaration

This article does not involve any human or animal subjects, and therefore does not require ethics approval

Acknowledgements

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Conflicts of Interest

No conflicts of interest in this work.


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Cite this article

Naik RB, Mangal D, Mathur A. Journal: Journal of Cardiovascular Medicine and Surgery Publication Date: July–December 2024 Volume/Issue: 10(3-4): 84-88


Licence:

Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)

This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator. 


Received Accepted Published
September 24, 2024 November 13, 2024 December 29, 2024

DOI: http://dx.doi.org/10.21088/jcms.2454.7123.103424.5

Keywords

Ebstenoid Tricuspid valveHypoplastic Right ventricleRight atrial clotOne and a half ventricle repairKays annuloplasty

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Received September 24, 2024
Accepted November 13, 2024
Published December 29, 2024

licence


Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)

This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator. 


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