Abstract

Turner syndrome, a chromosomal disorder characterized by partial or complete loss of X chromosome, presents unique challenges during pregnancy and anesthesia management due to associated comorbidities such as cardiac anomalies and musculoskelet al. abnormalities. A 30-year-old primigravid woman with mosaic Turner syndrome underwent an emergency cesarean section at 38 weeks and 2 days of gestation due to arrest at the second stage of labor with fet al. distress. The pregnancy was considered high-risk due to gestational hypertension, hypothyroidism, and premature rupture of membranes (PROM). Physical characteristics of Turner syndrome, such as short stature, low-set ears, and a broad chest, were present, though no major cardiac abnormalities were identified. Spinal anesthesia was administered using 2 ml of 0.5% bupivacaine, achieving a T5 sensory block. The procedure was uneventful, resulting in the delivery of a healthy male infant. Postoperative recovery was smooth, with no cardiac complications. This case emphasizes the importance of thorough preoperative evaluation, vigilant monitoring, and tailored anesthetic techniques to minimize risks.

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