Simmi K Ratan Director, Department of Pediatric Surgery, Maulana Azad Medical College, New Delhi 110002, India
Nitin Jain Assistant Professor,Department of Pediatric Surgery, Maulana Azad Medical College, New Delhi 110002, India
Shasanka Shekhar Panda Associate Professor, Department of Pediatric Surgery, Maulana Azad Medical College, New Delhi 110002, India
Sujoy Neogi Associate Professor, Department of Pediatric Surgery, Maulana Azad Medical College, New Delhi 110002, India
Address for correspondence: Simmi K Ratan, Director, Department of Pediatric Surgery, Maulana Azad Medical College, New Delhi 110002, India E-mail: drjohnsimmi@yahoo.com
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Nitin Jain, Simmi K Ratan, Shasanka Shekhar Panda, et al./An Extremely Rare Association of Prune belly Syndrome with Congenital Pouch colon : Case Report and Review of Literature/Pediatr Edu Res. 2022;10(1):23-27.
Timeline
Received : February 02, 2022
Accepted : April 07, 2022
Published : April 30, 2022
Abstract
Prune belly syndrome (PBS) is a triad of an abdominal wall muscular deficiency, cryptorchidism, and dilated urinary tract, and is often associated with other anomalies. Association of PBS with congenital pouch colon is extremely rare with only few handful of such reports in literature. We report here management of this rare associationin a male newborn with multiple genitourinary abnormalities.
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Data Sharing Statement
There are no additional data available. All raw data and code are available upon request.
Funding
This research received no funding.
Author Contributions
All authors contributed significantly to the work and approve its publication.
Ethics Declaration
This article does not involve any human or animal subjects, and therefore does not require ethics approval.
Acknowledgements
We would like to express our gratitude to the patients, their families, and all those who have contributed to this study.
Conflicts of Interest
No conflicts of interest in this work.
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Cite this article
Nitin Jain, Simmi K Ratan, Shasanka Shekhar Panda, et al./An Extremely Rare Association of Prune belly Syndrome with Congenital Pouch colon : Case Report and Review of Literature/Pediatr Edu Res. 2022;10(1):23-27.
This license enables
reusers to distribute, remix, adapt, and build upon the material in any medium
or format for noncommercial purposes only, and only so long as attribution is
given to the creator.
This license enables
reusers to distribute, remix, adapt, and build upon the material in any medium
or format for noncommercial purposes only, and only so long as attribution is
given to the creator.
Description: Showing (A, B & C)Type IV pouch colon lacking haustrations, appendices epiploicae, taenia coli with an abrupt transition from the normal proximal bowel to the distal dilated pouch was identified
Heading
Description: Showing (A)Enlarged and distended bladder with diverticulum, (B) Massively dilated ureter, (C) End descending colostomy, ureterostomy and suprapubic cystostomy
Heading
Description: Review of literature showing PBS with associated anomalies.