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An Extremely Rare Association of Prune belly Syndrome with Congenital Pouch colon : Case Report and Review of Literature

Simmi K Ratan, Nitin Jain, Shasanka Shekhar Panda, Sujoy Neogi

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Pediatric Education and Research 10(1):p 23-27, January-April 2022. | DOI: https://doi.org/10.21088/per.2321.1644.10122.3

How Cite This Article:

Nitin Jain, Simmi K Ratan, Shasanka Shekhar Panda, et al./An Extremely Rare Association of Prune belly Syndrome with Congenital Pouch colon : Case Report and Review of Literature/Pediatr Edu Res. 2022;10(1):23-27.

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Received : February 02, 2022         Accepted : April 07, 2022          Published : April 30, 2022

Abstract

Prune belly syndrome (PBS) is a triad of an abdominal wall muscular deficiency, cryptorchidism, and dilated urinary tract, and is often associated with other anomalies. Association of PBS with congenital pouch colon is extremely rare with only few handful of such reports in literature. We report here management of this rare associationin a male newborn with multiple genitourinary abnormalities.


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Data Sharing Statement

There are no additional data available. All raw data and code are available upon request.

Funding

This research received no funding.

Author Contributions

All authors contributed significantly to the work and approve its publication.

Ethics Declaration

This article does not involve any human or animal subjects, and therefore does not require ethics approval.

Acknowledgements

We would like to express our gratitude to the patients, their families, and all those who have contributed to this study.

Conflicts of Interest

No conflicts of interest in this work.


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Cite this article

Nitin Jain, Simmi K Ratan, Shasanka Shekhar Panda, et al./An Extremely Rare Association of Prune belly Syndrome with Congenital Pouch colon : Case Report and Review of Literature/Pediatr Edu Res. 2022;10(1):23-27.


Licence:

Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)

This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator.


Received Accepted Published
February 02, 2022 April 07, 2022 April 30, 2022

DOI: https://doi.org/10.21088/per.2321.1644.10122.3

Keywords

Congenital pouch colonPrune belly syndromeHigh Anorectal malformationMegaureter

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Received February 02, 2022
Accepted April 07, 2022
Published April 30, 2022

licence


Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)

This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator.


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