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Case Report

Airway and Anaesthetic Managment in Patients with Klippel-Treanunay Syndrome

Sushmitha S, Kiran N

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Indian Journal of Anesthesia and Analgesia 11(2):p 69-72, April - June 2024. | DOI: https://doi.org/10.21088/ijaa.2349.8471.11224.2

How Cite This Article:

Sushmitha S, Kiran N. Airway and anaesthetic management in patients with Klippel-Treanunay syndrome. Ind J Anesth Analg. 2024;11(2):69-72.

Timeline

Received : February 17, 2024         Accepted : April 22, 2024          Published : June 29, 2024

Abstract

Introduction: Klippel–Trenaunay syndrome is a rare sporadic condition described in terms of a clinical triad, Atypical lateral varicosity, Port wine stain (capillary malformation), Bone and soft tissue hypertrophy or hypotrophy. Case Report: We present a 20-year-old male, Non Vysya patient presented with history of pain in left ear and yellowish white sero-purulent discharge in the left ear since 10 days. On local examination there was discoloration over the left side of the face in the maxillary region, bifid tongue, swelling over the inner aspect of the left side of the mouth, the face was elongated with hypertrophy of the soft tissue of the left side of the face. Patient was diagnosed to have Left ear Chronic Otitis Media with postauricular abscess and was posted for Incision and drainage, canaloplasty, meatoplasty and excision of intraoral lesion. Anaesthesia was maintained with the help of Propofol, oxygen, nitrous oxide and vecuronium. Patient was fully awake and extubated, also we were able to see vocal cords movement during extubation. Patient was shifted to Post Anaesthesia Care Unit. Conclusion: Patients with Klippel–Trenaunay syndrome is rare condition needs thorough understanding of hemodynamic changes, proper preoperative assessment with vigilant intraoperative monitoring and management.


References

  • 1.   Lee J-H, Chung H-U, Lee M-S. An anesthetic management of a patient with Klippel-Trenaunay syndrome. Korean J Anesthesiol. 2012;63(1):90–1.
  • 2.   Marin RMP, Collada JCG, Martinez AIG, Serrano EMM, Aguilar JLM. Anesthetic management of Klippel-Trenaunay syndrome and attendant gastrointestinal hemorrhage. A case report. Minerva Anestesiol. 2007;73(3):187–90.
  • 3.   Tanaka Y, Sakamoto S-I, Bito H, Sakamoto A. Anaesthetic management of an abdominal aortic aneurysmorrhaphy in Klippel-Trenaunay-Weber syndrome: a case report. BMC Anesthesiol. 2022;22(1):214.
  • 4.   Gober-Wilcox JK, Gardner DL, Joste NE, Clericuzio CL, Zlotoff B. Limb hyperplasia: case report of an unusual variant of Klippel-Trenaunay syndrome and review of the literature. Cutis. 2009 May;83(5):255–62.
  • 5.   Barbara DW, Wilson JL. Anesthesia for surgery related to Klippel-Trenaunay syndrome: a review of 136 anesthetics. Anesth Analg. 2011 Jul;113(1):98–102.
  • 6.   George SE, Sreevidya A, Asokan A, Mahadevan V. Klippel Trenaunay syndrome and the anaesthesiologist. Indian J Anaesth. 2014;58(6):775–7.
  • 7.   Aronoff DM, Roshon M. Severe hemorrhage complicating the Klippel-Trénaunay-Weber syndrome. South Med J. 1998 Nov;91(11):1073–5.
  • 8.   Pereda Marin RM, Garcia Collada JC, Garrote Martinez AI, Miralles Serrano EM, Morales Aguilar JL. Anesthetic management of Klippel-Trenaunay syndrome and attendant gastrointestinal hemorrhage. A case report. Minerva Anestesiol. 2007 Mar;73(3):187–90.

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Funding

This research received no funding.

Author Contributions

All authors contributed significantly to the work and approve its publication.

Ethics Declaration

This article does not involve any human or animal subjects, and therefore does not require ethics approval.

Acknowledgements

Information not provided.

Conflicts of Interest

The authors report no conflicts of interest in this work.


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Cite this article

Sushmitha S, Kiran N. Airway and anaesthetic management in patients with Klippel-Treanunay syndrome. Ind J Anesth Analg. 2024;11(2):69-72.


Licence:

Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)

This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator.


Received Accepted Published
February 17, 2024 April 22, 2024 June 29, 2024

DOI: https://doi.org/10.21088/ijaa.2349.8471.11224.2

Keywords

Klippel-Trenaunay syndromePort wine stainVideo LaryngoscopyMalformations

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Received February 17, 2024
Accepted April 22, 2024
Published June 29, 2024

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Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)

This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator.


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