Yashif N A Post Graduate trainee, Department of Emergency Medicine, Max Superspeciality Hospital, Shalimar Bagh, Delhi 110088, India
Kishalay Datta Director and HOD, Department of Emergency Medicine, Max Superspeciality Hospital, Shalimar Bagh, Delhi 110088, India
Priya Govil Associative Consultant, Department of Emergency Medicine, Max Superspeciality Hospital, Shalimar Bagh, Delhi 110088, India
Shebin Althaf Resident, Department of Emergency Medicine, Max Superspeciality Hospital, Shalimar Bagh, Delhi 110088, India
Address for correspondence: Yashif N A, Post Graduate trainee, Department of Emergency Medicine, Max Superspeciality Hospital, Shalimar Bagh, Delhi 110088, India E-mail: yashifbava2010@gmail.com
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Yashif N A, Kishalay Datta, Priya Govil, et al./Pharyngeal-Cervical-Brachial Variant of Guillain Barre Syndrome/Indian J Emerg Med 2023;9(1):33–35.
Timeline
Received : October 20, 2022
Accepted : November 25, 2022
Published : March 30, 2023
Abstract
Guillain-Barre Syndrome (GBS) usually present as1 symmetrical ascending muscle weakness associated with
areflexia and flaccidity with or without sensory symptoms. However,2 in some patients it may present atypically
and one of the rare variant is Pharyngeal-cervical-brachial variant, usually presented as muscle weakness extending
from cervical area to the upper extremities often affected with proximal muscle groups. A 20-year-old male presented in ER with complaints of weakness over bilateral upper limb, dysphagia and difficulty in speaking followed by quadriparesis and breathing difficulty. Diagnosis of PCB variant was made by CSF and nerve conduction study and all other possible differentials were excluded. The patient improved by administration of iv immunoglobulin and other supportive measures. Physician should think about PCB variant of GBS, whenever a patient presenting with symmetrical upper limb weakness and bulbar palsy.
References
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Data Sharing Statement
There are no additional data available. All raw data and code are available upon request.
Funding
This research received no funding.
Author Contributions
All authors contributed significantly to the work and approve its publication.
Ethics Declaration
This article does not involve any human or animal subjects, and therefore does not require ethics approval.
Acknowledgements
We would like to express our gratitude to the patients, their families, and all those who have contributed to this study.
Conflicts of Interest
No conflicts of interest in this work.
About this article
Cite this article
Yashif N A, Kishalay Datta, Priya Govil, et al./Pharyngeal-Cervical-Brachial Variant of Guillain Barre Syndrome/Indian J Emerg Med 2023;9(1):33–35.
This license
enables reusers to distribute, remix, adapt, and build upon the material in any
medium or format for noncommercial purposes only, and only so long as
attribution is given to the creator.
This license
enables reusers to distribute, remix, adapt, and build upon the material in any
medium or format for noncommercial purposes only, and only so long as
attribution is given to the creator.