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Indian Journal of Anesthesia and Analgesia 11(3):p 165-167, July- September 2024. | DOI: https://doi.org/10.21088/ijaa.2349.8471.11324.10
Case Report
Anaesthetic Management of Gaucher Disease for Splenectomy
Dixsha T P, S. Mohideen Abdul Kadar, Aneesh Rajan, Sasidharan Nair M
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Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator.
Indian Journal of Anesthesia and Analgesia 11(3):p 165-167, July- September 2024. | DOI: https://doi.org/10.21088/ijaa.2349.8471.11324.10
How Cite This Article:
Dixsha TP, Kadar SMA, Rajan A, et al. Anaesthetic management of Gaucher disease for splenectomy. Ind J Anesth Analg. 2024;11(3):165-7.Timeline
Received : April 08, 2024
Accepted : September 27, 2024
Published : September 28, 2024
Abstract
Gaucher`s disease is the most common form of lysosomal storage disorder. It is caused by an inherited deficiency of beta glucocerebrosidase enzyme. It results in accumulation of beta glucocerebroside leading to end organ dysfunction. Gaucher disease is an autosomal recessive inheritance by mutations in the GBA gene on chromosome 1. It affects both sexes. The incidence is estimated to be 1:40000 in Europe. Most commonly, the disease is differentiated into a non-neuronopathic form and a neuronopathic form. Gaucher disease may present a challenge to the anesthesiologist because of abnormal coagulation and multi organ dysfunction. These factors may affect the choice of anaesthesia type. We aim to report the anaesthetic management in a 25 years old male with Gaucher’s disease posted for splenectomy.
References
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Funding
This research received no funding.
Author Contributions
All authors contributed significantly to the work and approve its publication.
Ethics Declaration
This article does not involve any human or animal subjects, and therefore does not require ethics approval.
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Conflicts of Interest
The authors report no conflicts of interest in this work.
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Cite this article
Dixsha TP, Kadar SMA, Rajan A, et al. Anaesthetic management of Gaucher disease for splenectomy. Ind J Anesth Analg. 2024;11(3):165-7.
Licence:
Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator.
| Received | Accepted | Published |
|---|---|---|
| April 08, 2024 | September 27, 2024 | September 28, 2024 |
DOI: https://doi.org/10.21088/ijaa.2349.8471.11324.10
Keywords
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Timeline
| Received | April 08, 2024 |
| Accepted | September 27, 2024 |
| Published | September 28, 2024 |
licence
Attribution-Non-commercial 4.0 International (CC BY-NC 4.0)
This license enables reusers to distribute, remix, adapt, and build upon the material in any medium or format for noncommercial purposes only, and only so long as attribution is given to the creator.
