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Ranajit Naik, Mangal D , Mathur A. One and a Half Ventricle Repair of a Rare Ebstenoid Tricuspid Valve Orifice with a Hypoplastic Right Ventricle. J Cardiovasc Med Surg.2024;10(3-4):84-88.
Timeline
Received : September 24, 2024
Accepted : November 13, 2024
Published : December 30, 2024
Abstract
Primary tricuspid valve disease related to its congenital malformation is rare. Ebstein’s anamoly is a rare congenital condition affecting the septal and posterior leaflets of the tricuspid valve. Ebstein’s anamoly has a wide spectrum of pathological features. We describe the case of 33 year old female with Ebsteinoid tricuspid valve orifice, severely hypoplastic right ventricle and thrombus in a giant right atrium, with intact interatrial and interventricular septa. The patient was managed surgically with Kays tricuspid annuloplasty and right Bidirectional Glenn anastomosis constituting one and a half ventricular repair with satisfactory outcome.
References
1. Keith JB, Rows RD, Vlad P. Heart disease in infancy and childhood. Academic Medicine. 1958;33(8):608.
2. Schreiber C, Cook A, Ho SY, Augustin N, Anderson RH. Morphologic spectrum of Ebstein's malformation: revisitation relative to surgical repair. J ThoracCardiovasc Surg. 1999 Jan;117(1):148-55. doi: 10.1016/s0022-5223(99)70480-0. PMID: 9869769.
3. Betigeri, V., Niwariya, Y., Modi, P. et al. Congenitally unguarded tricuspid valve orifice with a hypoplastic right ventricle and free thrombus in a giant right atrium. Indian J ThoracCardiovascSurg 23, 272–274 (2007). https://doi.org/10.1007/s12055-007-0058-x
4. ChauvaudS.Ebstein'smalformation.Surgical treatment and results.ThoracCardiovasc Surg. 2000; 48: 220-223.
5. Perloff ’s clinical recognition of congenital heart disease. 6th edition. pp. 92–176.
6. S. Chauvaud, A. Berrebi, N. d'Attellis, E. Mousseaux, A. Hernigou, A. Carpentier, Ebstein's anomaly: repair based on functional analysis, European Journal of Cardio-Thoracic Surgery, Volume 23, Issue 4, April 2003, Pages 525–531, https://doi.org/10.1016/ S1010-7940(02)00836-9
7. Kay JH, Maselli-Campagna G, Tsuji HK: Surgical treatment of tricuspid insufficiency. Ann Surg 162:53, 1965
8. Talwar, S., Siddharth, B., Choudhary, S.K. et al. One and half ventricle repair: rationale, indications, and results. Indian J ThoracCardiovascSurg 34, 370–380 (2018). https://doi.org/10.1007/s12055-017-0628-5
Data Sharing Statement
There are no additional data available. All raw data and code are available upon request.
Funding
This research received no funding.
Author Contributions
All authors contributed significantly to the work and approve its publication.
Ethics Declaration
This article does not involve any human or animal subjects, and therefore does not require ethics approval.
Acknowledgements
We would like to express our gratitude to the patients, their families, and all those who have contributed to this study.
Conflicts of Interest
No conflicts of interest in this work.
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Cite this article
Ranajit Naik, Mangal D , Mathur A. One and a Half Ventricle Repair of a Rare Ebstenoid Tricuspid Valve Orifice with a Hypoplastic Right Ventricle. J Cardiovasc Med Surg.2024;10(3-4):84-88.
This license enables
reusers to distribute, remix, adapt, and build upon the material in any medium
or format for noncommercial purposes only, and only so long as attribution is
given to the creator.
This license enables
reusers to distribute, remix, adapt, and build upon the material in any medium
or format for noncommercial purposes only, and only so long as attribution is
given to the creator.