Gananjay G. Salve Chief Consultant, Department of Cardiovascular and Thoracic Surgery, KLES Dr. Prabhakar Kore Hospital and Medical Research Centre, Belgaum 590010, India
Shreepal A. Jain Consultant, Department of Paediatric Cardiology, BJ Wadia Hospital for Children, Mumbai, Maharashtra 400014, India
Bharat V. Dalvi Senior Consultant, Department of Pediatric Cardiac Sciences, Sir H.N. Reliance Foundation Hospital, Mumbai, Maharashtra 400004, India
Krishnanaik Shivaprakash Head of Department, Department of Pediatric Cardiac Sciences, Sir H.N. Reliance Foundation Hospital, Mumbai, Maharashtra 400004, India
Address for correspondence: Gananjay G. Salve, Chief Consultant, Department of Cardiovascular and Thoracic Surgery, KLES Dr. Prabhakar Kore Hospital and Medical Research Centre, Belgaum 590010, India E-mail: gananjay.salve@gmail.com
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Gananjay G. Salve, Shreepal A. Jain, Bharat V. Dalvi, Krishnanaik Shivaprakash. Simultaneous Atrioventricular Valve Repair
Compelling Creation of Unconventional Fenestration During Extracardiac Total Cavopulmonary Connection. J Cardiovasc Med Surg.2024;10(1-2):39-42.
Timeline
Received : February 26, 2024
Accepted : June 25, 2024
Published : June 30, 2024
Abstract
Severe regurgitation of the atrio-ventricular valve and borderline pulmonary vascular resistance are risk factors for failure of univentricular repair. We believe that fenestration in the Fontan pathway plays an important role in avoiding postoperative catastrophesimmediate and late, in such high-risk substrates. Rarely, the intra-operative circumstances compel the surgeon to opt for an unconventional method of fenestration. We report an interesting case of high-risk univentricular repair, had previously undergone pulmonary artery banding and bidirectional Glenn shunt, who now required a simultaneous repair of the regurgitant atrio-ventricular valve compelling the creation of an unconventional fenestration during Stage III palliation.
References
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Data Sharing Statement
There are no additional data available. All raw data and code are available upon request.
Funding
This research received no funding.
Author Contributions
All authors contributed significantly to the work and approve its publication.
Ethics Declaration
This article does not involve any human or animal subjects, and therefore does not require ethics approval.
Acknowledgements
We would like to express our gratitude to the patients, their families, and all those who have contributed to this study.
Conflicts of Interest
No conflicts of interest in this work.
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Cite this article
Gananjay G. Salve, Shreepal A. Jain, Bharat V. Dalvi, Krishnanaik Shivaprakash. Simultaneous Atrioventricular Valve Repair
Compelling Creation of Unconventional Fenestration During Extracardiac Total Cavopulmonary Connection. J Cardiovasc Med Surg.2024;10(1-2):39-42.
This license enables
reusers to distribute, remix, adapt, and build upon the material in any medium
or format for noncommercial purposes only, and only so long as attribution is
given to the creator.
This license enables
reusers to distribute, remix, adapt, and build upon the material in any medium
or format for noncommercial purposes only, and only so long as attribution is
given to the creator.
Description: This is a sagittal view of contrast-enhanced computerized tomography scan showing widely patent superior cavo-pulmonary connection (short arrow) and banded main pulmonary artery (long arrow). One can appreciate the absence of interventricular septum, and the tiny collateral vessels around the heart. Ao Aorta; MPA Main pulmonary artery; SV Single ventricle; SVC Superior vena cava.
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Description: This is an intraoperative photograph taken from the head-end of the patient, showing the heart in diastolic cardioplegic arrest and ascending aorta cross-clamped. The right atrium is opened and retracted with stay sutures. The right atrioventricular (AV) valve is being repaired (arrow). Pericardial adhesions can be noted.
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Description: This is another intraoperative photograph taken from the right side of the patient, showing the extracardiac expanded polytetrafluoroethylene conduit anastomosed to the distal open end of the inferior vena cava. Kreutzer’s technique of fenestration (arrow) has been performed, wherein the proximal open end of the inferior vena cava is sutured to an opening made in the adjacent part of the extracardiac Fontan conduit.
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Description: Postoperative echocardiography (2-dimensional and colour doppler) in short axis view showing well-functioning and competent both atrioventricular (AV) valves and good flow in the Kreutzer’s fenestration communicating to the Fontan conduit. The absence of interventricular septum amounting to a single ventricle also can be appreciated in this view.
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Description: Postoperative echocardiography (2-dimensional and colour doppler) in long axis view showing patent extracardiac Fontan conduit (short arrow) sutured to the inferior vena cava (IVC) and good flow in the Kreutzer’s fenestration (long arrow).