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DOI: DOI: http://dx.doi.org/10.21088/ijmfnm.2347.999X.5218.13

Abstract

Background: Pierre Robin syndrome (PRS) is characterised by micrognathia (undersized jaw), glossoptosis (retracted tongue), and airway obstruction. Neonates with a complete type of cleft palate, frequently present with feeding problems and aspiration is a common compliction. Presented here are two cases with Pierre Robin Syndrome. Case summary: First case is a 3 month male with feeding difficulty and aspiration pneumonia had receding chin and cleft palate on examination. He was feed by nasogastric tube initially and later a obturator was fitted. Second case is a 6 month female with bronchpneumonia and had a high arched, U shaped cleft palate and a large tongue. Conclusion: Early diagnosis for proper feeding and growth of children with Pierre Robin Syndrome is important to prevent complications like failure to thrive and repeated aspiration pneumonia.

Keywords: Pierre Robin Syndrome; Micrognathia; Cleft Palate.

 

Corresponding Author : 1Resident, 2Professor and Head, 3Assistant Professor, 4Principal and Professor, Department of Paediatrics, DVVPF’s Medical College, Ahmednagar Maharashtra 414111, India.