Fibrous Dysplasia is a benign, non-familial condition in which normal bone is replaced by fibrous tissue and woven bone. It rarely effects temporal bone. The diagnosis is usually based on clinical, radiographic, and histopathologic features. We here present a case of secondary cholesteatoma caused by external auditory canal occlusion by fibrous dysplasia which was successfully treated by radical mastoidetomy and partial cavity reconstruction by muscle periosteal flap with adequate meatoplasty.

Keywords: Fibrous Dysplasia; Monostotic; Polystotic; Temporal Bone.