Context: In general, congenital heart defects are classified as single, complex and undifferentiated. Aim: The present study is reporting the types of congenital heart defects that were observed in 65 patients. Methods and Material: There were 33 males and 32 females and their age ranged from neonate to 16 years. For the gathered information, percentage analysis was calculated. Results: It is seen that congenital heart defects as single entity was present in 36 (55.5%) cases; complex in 14 (21.5%) and undifferentiated in 15 (23%). In 32 female patients, congenital heart defects as single were present in 21 (65.6%), complex in 5 (15.7%) and undifferentiated in 6 (18.7%); whereas they were 15 (45.4%), 9 (27.3%) and 9 (27.3%) respectively in male patients. In female, it is observed, that atrial and ventricular septal defects were 6 and 5; but in male they were 3 and 4. Patent foramen ovale and atrio ventricular canal defects were not observed in female and in the males, dextrocardia and coarctation of aorta were not seen. Conclusion: In the present study, even though for the total, the association could be elicited between the female patients and CHDs; in male patients the occurrence of the complex CHDs were associated. Genetic counseling for the diagnosis, recurrence risk and medical management are provided.

Keywords: Congenital; Atrial; Ventricular Septal; Dextrocardia.