AbstractRhabdomyosarcoma (RMS), a cancer of connective tissue is the most common soft tissue sarcoma of childhood and adolescence. Head and neck region is being most common site followed by genitourinary tract, retroperitonium, and the extremities. After neuroblastoma and Wilms tumor, RMS is the third most common extra cranial malignant tumor that affects childhood age group. These tumors arise from mesenchymal tissue(skeletal muscle progenators) with a tendency of myogenic differentiation. Morphologically, RMS are classified into embryonal RMS, alveolar, undifferentiated and anaplastic RMS. Alveolar type is the most common type. Recently various treatment modalities for rms are introduced which has increased the survival of patients with RMS and some investigators have associated the prognosis with the location, evolution and histological type and spread of the tumor. RMS are also associated with high rates of recurrence and metastasis. Here we present a case report of RMS over posterior chest wall in a 6 months old female child .