Ebstein’s anomaly is a rare congenital heart disease, which involves downward displacement of tricuspid valve and atrialisation of right ventricle associated with either atrial septal defect or patent foramen ovale through which shunting of blood occurs. In such patient, clinical presentation varies from congestive cardiac failure in childhood to incidental diagnosis in adulthood. If such patient presents with fracture neck of femur, it will be a challenging job for orthopaedic surgeon as well as anaesthesiologist. The main goals of treatment are to stabilize the hip, decrease pain and restore the level of pre-fracture function with minimal operative intervention.

Keywords: Ebstein’s anomaly; intra-capsular femur neck fractures; hemi-replacement arthroplasty; avascular necrosis; epidural anaesthesia.