Oesophageal achalasia is a idiopathic disorder characterized by abnormal motility and failure of relaxation of lower esophageal sphincter, with its usual presentation in young adults. It is an uncommon disease in childhood and extremely rare under the age of one year. We are reporting a case of a 1 year female who presented with persistant vomitting and was diagnosed of having with Achalasia Cardia with barium swallow and was treated with Heller’s Modified Cardiomyotomy.

Keywords: Achalasia Cardia; Heller’s Cardiomyotomy