Odontogenic myxoma(OM) is a rare and locally invasive benign neoplasm found exclusively in the jaws. OM is predominantly found in young adults, and most of the time mandible is involved. OMs are lesions with extremely varied clinical and radiographic characteristic and the diagnosis is therefore not easy. We report an interesting case of OM with extensive involvement of maxillary sinus and upper jaw in a hemophilic patient. A brief review of relevant literature is included.No recurrence was found after one year follow up.

Key words: Odontogenic tumors, Odontogenic myxoma, maxillary Sinus,case report