Introduction: Fahr’s syndrome is a rare, degenerative neurological idiopathic condition characterized by basal ganglia calcification. It often appears between 40 - 60 years of age and can occasionally be seen in children. Case Report: In our case, it was a 40 year old female who presented with seizures and lab investigation showed-hypocalcemia & hypothyroidism. On Computed Tomography (CT) study, bilateral symmetrical calcifications in centrum semiovale, corona radiata, subcortical white matter of fronto parietal regions, caudate & lentiform nuclei and cerebellum were noted. Conclusion: Patients presenting with seizures and laboratory investigations showing hypocalcemia and abnormal parathyroid hormone levels, detailed neurological clinical examination and Computed tomography should be performed to rule out any abnormal intracranial calcification.