Abstract Desmoid tumor (musculoaponeurotic fibromatosis) is an aggressive monoclonal fibroblastic proliferation arising in musculo-aponeurotic structure at any site. It is a distinct pathological entity which can locally infiltrate and recur posing therapeutic challenges to a surgeon. We are reporting a rare case of abdominal desmoid tumor in a young patient.
Keywords: Desmoid; Abdomen; Fibroblast.