Idiopathic intracranial hypertension (IIH) or Benign intracranial hypertension (BIH) is an uncommon disorder  characterized by signs and symptoms of raised intracranial pressure of unknown cause and usually without any  evidence of intracranial pathology. This condition typically affects obese women. The incidence of IIH is increasing  with the rising prevalence of obesity. The most common symptoms are headache, nausea, vomiting, pulsatile  tinnitus, transient episodes of visual loss, diplopia and other visual symptoms. Papilledema is a major clinical sign.  Visual impairment is a serious complication that may not be recognized by the patients. As its presenting symptoms  mimic those of a brain tumour, it’s also called pseudotumor cerebri (PTC). This paper in brief reviews epidemiology,  clinical manifestations, etiopathogenetic hypothesis, diagnostic challenges, and current treatments of IIH including  medical, surgical, and interventional management of this condition. The efficacy and complications of surgical  interventions like cerebrospinal fluid diversion, optic nerve sheath fenestration, and endovascular venous stenting  reported in recent two to three decades have been summarized in brief.