Malrotation is not a common condition in relation to kidney and can present with certain problems during different surgical procedures. A proper knowledge of Anatomy of Kidneys is important . The condition has been associated with many other clinical conditions like accessory or aberrant vessels and in relation to certain distinctive syndromes.we present a rare case of Malrotation of Left Kidney with Accessory Lower Renal artery

Keywords: Metanephros; Kidney; Malrotation.