Mucinous cystadenoma of the appendix is a rare benign tumor of appendix. Histopathologically divided into three groups: focal or diffuse mucosal hyperplasia, mucinous cystadenoma and mucinous cystadenocarcinoma. This condition is often associated with other neo-plasia, especially adenocarcinoma of the colon and ovaries. In this case report we discuss a case of a 48 yearold male diagnosed with mucinious cystadenoma of the appendix treated successfully. We have added the pathology, various diagnostic modalities and treatment for the above mentioned disorder.