Hirayama’s disease is a rare focal motor neuron disease that is reported mainly in young Asian males (15-25 years old). Hirayama disease also known as juvenile non-progressive cervical myotrophy or monomelic amyotrophy. Insidious onset and slow progression of weakness followed by a spontaneous arrest within several years are classical symptoms described with disease. MRI cervical spine in flexion is mainstay for diagnosis.

Keywords: Hirayama Disease (Hd); Cervical Myelopathy; Juvenile Non-Progressive Cervical Myotrophy